Varegacestat in Desmoid Tumors
- An NDA seeking the approval of investigational, once-daily gamma secretase inhibitor varegacestat for the treatment of adult patients with desmoid tumors has been submitted to the FDA.
- The phase 3 RINGSIDE trial met its primary end point, showing an 84% reduction in the risk of disease progression or death with varegacestat vs placebo.
- Varegacestat was generally well tolerated, with a manageable safety profile consistent with the gamma secretase inhibitor class.
How was RINGSIDE designed?
RINGSIDE was a global, randomized, double-blind trial that enrolled adult patients with progressing desmoid tumors.1,2 Patients were also required to have at least 1 measurable lesion amenable to volume measurements by MRI at screening and have recurrent/refractory disease after at least 1 line of therapy, including surgery, radiation, or systemic therapy.2 Of note, patients who were treatment naive could receive varegacestat if deemed appropriate by the investigator.
The study included 156 patients who were randomly assigned to receive either varegacestat at 1.2 mg daily or placebo until disease progression or death.1 This population represents the largest of its kind to be assessed in a randomized trial, according to Immunome.
The primary end point was PFS as assessed by BICR. Secondary end points included ORR per RECIST 1.1 criteria and change in tumor volume at week 24 per BICR, change in pain intensity at week 12, duration of response, best reduction in tumor volume, patient-reported outcomes, and safety and tolerability.
RINGSIDE includes an ongoing open-label extension phase.
What was the safety profile of varegacestat?
Topline safety data from RINGSIDE demonstrated that varegacestat was generally well tolerated, with a manageable safety profile consistent with the gamma secretase inhibitor class.1 The most common any-grade adverse effects (AEs) in the investigational arm included diarrhea (82%), fatigue (44%), rash (43%), nausea (35%), and cough (34%). Most AEs were grade 1 or 2 in severity.
Data from RINGSIDE were selected for presentation in an oral abstract session at the 2026 American Society of Clinical Oncology Annual Meeting, according to Immunome.
References
- Immunome announces submission of new drug application to US FDA for varegacestat for the treatment of adults with desmoid tumors. News release. Immunome. April 29, 2026. Accessed April 29, 2026. https://investors.immunome.com/immunome-announces-submission-of-new-drug-application-to-u-s-fda-for-varegacestat-for-the-treatment-of-adults-with-desmoid-tumors/
- A study of AL102 in patients with progressing desmoid tumors (RINGSIDE). CliinicalTrials.gov. Updated February 5, 2026. Accessed April 29, 2026. https://clinicaltrials.gov/study/NCT04871282